Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia

Authors

• Alamelu Alagappan, Department of Radiodiagnosis, All India institute of medical sciences, Bhubaneswar, Odisha, India
• Biswajit Sahoo, Department of Radiodiagnosis, All India institute of medical sciences, Bhubaneswar, Odisha, India
• Jain H. Panigrahi, Department of Gastroenterology, All India institute of medical sciences, Bhubaneswar, Odisha, India
• Manas K., Department of Gastroenterology, All India institute of medical sciences, Bhubaneswar, Odisha, India
• Taraprasad Tripathy, Department of Radiodiagnosis, All India institute of medical sciences, Bhubaneswar, Odisha, India

Abstract

Hereditary haemorrhagic telangiectasia (HHT) is an autosomal dominant disorder characterised by vascular dysplasia. Hepatic vascular m alformations (VMs) range from small telangiectases to significant vascular shunting. Here we report two cases of HHT. Case 1 had diffuse ectasia of the hepatic artery along its intrahepatic and extrahepatic course with a hepatic arterial aneurysm. Case 2 presented with ileal and hepatic telangiectases. Knowledge of these vascular variants is indispensable for clinicians and radiologists in aiding diagnosis and surgical and interventional management.

Article Type

Case Report

Publication Date

11-30-2023

First Page

551

Last Page

555

Creative Commons License

This work is licensed under a Creative Commons Attribution-No Derivative Works 4.0 International License.

Recommended Citation

Alagappan, Alamelu; Sahoo, Biswajit; Panigrahi, Jain H.; Manas K.; and Tripathy, Taraprasad (2023) "Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia," Sultan Qaboos University Medical Journal: Vol. 23: 551-555.
DOI: https://doi.org/10.18295/squmj.1.2023.011